Table 1. Anatomical Involvement. Display of the anatomical location of skin lesions (Upper Extremity, Lower Extremity, Trunk, Face, Ears, Nose, and Oral), as well as joint involvement as manifested by arthralgias.

 

Author

No. Cases

Upper Extremity

Lower Extremity

Trunk

Face

Ears

Nose

Oral

Arthralgias

Ching et al12

1

1/1

1/1

0/1

1/1

0/1

1/1

0/1

0/1

Jacob et al21

2

1/2

1/2

1/2

1/2

2/2

0/2

0/2

0/2

Ulrich et al9

5

3/5

5/5

2/5

1/5

3/5

0/5

0/5

4/5

Zwang et al10

1

1/1

1/1

1/1

0/1

1/1

0/1

1/1

1/1

Fthenakis & Klein22

1

0/1

1/1

1/1

1/1

1/1

1/1

0/1

0/1

Mouzakis et al23

1

1/1

1/1

1/1

1/1

1/1

1/1

0/1

0/1

Gross et al24

4

3/4

3/4

1/4

1/4

1/4

0/4

0/4

3/4

Click25

1

0/1

1/1

0/1

0/1

0/1

0/1

0/1

0/1

Chung et al11

6

4/6

5/6

3/6

3/6

6/6

1/6

0/6

0/6

Reutemann et al5

1

1/1

1/1

0/1

0/1

1/1

0/1

0/1

0/1

Bradford et al4

2

0/2

1/2

0/2

2/2

2/2

0/2

0/2

1/2

Walsh et al2

2

2/2

1/2

2/2

0/2

0/2

0/2

0/2

1/2

Jenkins et al6

1

0/1

1/1

1/1

1/1

1/1

0/1

1/1

0/1

Dy et al7

1

0/1

1/1

1/1

0/1

1/1

0/1

0/1

1/1

Farhat et al26

2

1/2

2/2

1/2

0/2

0/2

1/2

0/2

0/2

Geller et al27

1

1/1

1/1

1/1

0/1

1/1

0/1

0/1

1/1

John et al28

1

1/1

1/1

1/1

0/1

0/1

0/1

0/1

0/1

Waller et al29

2

2/2

2/2

0/2

1/2

2/2

0/2

0/2

0/2

UMMC Cases

4

3/4

4/4

3/4

4/4

3/4

1/4

1/4

0/4

Graf et al30

6

6/6

6/6

0/6

6/6

6/6

0/6

0/6

0/6

Han et al31

1

1/1

1/1

0/1

1/1

1/1

1/1

0/1

0/1

De la Hera et al32

1

0/1

0/1

0/1

0/1

1/1

0/1

0/1

1/1

Poon et al8

4

0/4

3/4

1/4

1/4

3/4

1/4

1/4

3/4

Khan et al33

4

2/4

2/4

1/4

1/4

3/4

0/4

0/4

1/4

Totals

55

34/55

46/55

22/55

26/55

40/55

21/55

4/55

17/55