Table 2. Summary of tools available for the assessment of skin disease in the IIM*.

 

 

Name

 

 

Abbreviation

Global Tool or Independent Skin Assessment

 

Subgroup validated

 

 

Validation

Disease Activity Score

DAS

Part of Global Tool

JDM

Reliability, Construct validity, Responsiveness

Myositis Disease Activity Assessment

MYOACT

Part of Global Tool

JDM, DM, PM

Responsivene

Myositis Intention-to-Treat Activity Index

MITAX

Part of Global Tool

JDM, DM, PM

Responsiveness

Cutaneous Assessment Tool

CAT

Independent Skin Assessment

JDM

Reliability, Construct  Validity, Responsiveness

Dermatomyositis Skin Severity Index

DSSI

Independent Skin Assessment

JDM, DM

Reliability, Construct Validity

Cutaneous Dermatomyositis Disease Area and Severity Index

CDASI

Independent Skin Assessment

DM, ADM

Reliability, Construct Validity

 

* Abbreviations:

IIM = idiopathic inflammatory myopathies
JDM = juvenile dermatomyositis
DAS = Disease Activity Score
MYOACT = Myositis Disease Activity Assessment Tool, Visual Analog Scale version
MITAX = Myositis Intention-to-Treat Activity Index
CAT = Cutaneous Assessment Tool
DSSI = Dermatomyositis Skin Severity Index
CDASI = Cutaneous Dermatomyositis Disease Area and Severity Index
DM = dermatomyositis
PM = polymyositis
ADM = amyopathic dermatomyositis